Primitive Neuroectodermal Tumors

A group of malignant tumors of the nervous system that feature primitive cells with elements of neuronal and/or glial differentiation. Use of this term is limited by some authors to central nervous system tumors and others include neoplasms of similar origin which arise extracranially (i.e., NEUROECTODERMAL TUMORS, PRIMITIVE, PERIPHERAL). This term is also occasionally used as a synonym for MEDULLOBLASTOMA. In general, these tumors arise in the first decade of life and tend to be highly malignant. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2059)

Also Known As:

PNET; Primitive Neuroectodermal Tumor; Ependymoblastoma; Tumor, Primitive Neuroectodermal; Spongioblastoma; Neuroectodermal Tumors, Primitive; Cerebral Primitive Neuroectodermal Tumor; Neoplasms, Primitive Neuroepithelial; Neuroectodermal Tumor, Primitive; Neuroepithelial Neoplasms, Primitive; Primitive Neuroepithelial Neoplasms; Ependymoblastomas; Medulloepitheliomas; Neoplasm, Primitive Neuroepithelial; Neuroepithelial Neoplasm, Primitive; Neuroepithelial Tumor, Primitive; PNETs; Primitive Neuroepithelial Neoplasm; Primitive Neuroepithelial Tumor; Primitive Neuroepithelial Tumors; Spongioblastomas; Tumor, Primitive Neuroepithelial; Tumors, Primitive Neuroectodermal; Tumors, Primitive Neuroepithelial; Medulloepithelioma; Neuroepithelial Tumors, Primitive

Neoplasms: 1324753
- Neoplasms by Histologic Type: 2
  - Germ Cell and Embryonal Neoplasms: 4454
    - Neuroectodermal Tumors: 217
      - Neuroepithelial Neoplasms: 412
        Primitive Neuroectodermal Tumors: 1966
  - Glandular and Epithelial Neoplasms: 439
    - Neuroepithelial Neoplasms: 412
      - Primitive Neuroectodermal Tumors: 1966
  - Nerve Tissue Neoplasms: 1
    - Neuroectodermal Tumors: 217
      - Neuroepithelial Neoplasms: 412
        Primitive Neuroectodermal Tumors: 1966

Children's Cancer and Leukaemia Group CNS Tumour Division Selected Research

Children's Cancer and Leukaemia Group CNS Tumour Division Research Topics

Disease

Therapy/Procedure